Abstract

Left ventricular noncompaction is a relatively newly recognized cardiomyopathy with morphological characteristics of excessive trabeculations and deep recesses. Clinical outcomes for this disease range widely from no symptoms to life-threatening arrhythmia, cardiac failure, thromboembolism, and sudden cardiac death. We report an interesting sporadic case with left ventricular noncompaction, diagnosed in a 14-yearold before symptoms emerged, showing deteriorating during adolescence, and eventually necessitating heart transplantation. This sporadic, juvenile, asymptomatic case would be considered low risk in a previous study, but the underlying left ventricular dysfunction was classified as high risk. After initial improvement, ventricular dysfunction deteriorated again after drug compliance worsened. Left ventricular noncompaction is a rare, heterogeneous disease. Each case should be treated carefully and followed-up.